Additional file 1: of Satellite cells maintain regenerative capacity but fail to repair disease-associated muscle damage in mice with Pompe disease

Schaaf, Gerben; van Gestel, Tom; in ‘t Groen, Stijn; de Jong, Bart; Boomaars, Björn; Tarallo, Antonietta; Cardone, Monica; Parenti, Giancarlo; van der Ploeg, Ans; Pijnappel, W.

doi:10.6084/m9.figshare.7313774.v1

40478_2018_620_MOESM1_ESM.pdf (122.7 kB)

Additional file 1: of Satellite cells maintain regenerative capacity but fail to repair disease-associated muscle damage in mice with Pompe disease

journal contribution

posted on 2018-11-07, 05:00 authored by Gerben Schaaf, Tom van Gestel, Stijn in ‘t Groen, Bart de Jong, Björn Boomaars, Antonietta Tarallo, Monica Cardone, Giancarlo Parenti, Ans van der Ploeg, W. Pijnappel

Figure S1. Reduced fiber diameter in GAAKO animals. A. Fiber diameter frequency distribution plot of WT(FVB) and Gaa−/−(FVB) at 15 weeks of age. B. WT(Bl6) and GAAKO(Bl6) at 3 months of age showing reduced fiber diameter in Gaa−/− (Bl6). These data suggest muscle atrophy is observed in GAA-deficient animals on both FVB/N and C57/Bl6 backgrounds. (PDF 122 kb)

Funding

Prinses Beatrix Spierfonds

History

Usage metrics

Keywords

Satellite cells Muscle regeneration Pompe disease Lysosomal storage disease Glycogenosis type II

Licence

CC BY + CC0

Exports

RefWorks

BibTeX

Ref. manager

Endnote

DataCite

NLM

DC

Additional file 1: of Satellite cells maintain regenerative capacity but fail to repair disease-associated muscle damage in mice with Pompe disease

Funding

Prinses Beatrix Spierfonds

History

Usage metrics

Categories

Keywords

Licence

Exports