Anthropomorphic and cardiac magnetic resonance data in subjects with Friedreich ataxia.
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posted on 2024-05-30, 17:27 authored by Roger E. Peverill, Kimberly Y. Lin, Mark A. Fogel, Michael M. H. Cheung, W. Stuart Moir, Louise A. Corben, Glenn Cahoon, Martin B. DelatyckiAnthropomorphic and cardiac magnetic resonance data in subjects with Friedreich ataxia.
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native t1 timemales ), 9localised replacement fibrosislate gadolinium enhancementgaa repeat lengthdiffuse myocardial fibrosiscardiac magnetic resonanceextracellular volume fractionlv structural changelv replacement fibrosislv ejection fractionindependent positive correlationfrda genetic severitygenetic severitynegative correlationdiastolic volumeassociations independentlv massxlink ">standard measurementssimilar relationshipsreduced lvefpositively correlatednormal rangenormal lveflvef ).left ventricularfxn friedreich ataxiaassessed using5t scanner55 %).39 %,22 %,
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