Marfan Syndrome: Single-Stage Surgical Repair of Pectus Excavatum Combined With Mitral Valve Repair and David Procedure

A 29-year-old male with a known history of Marfan syndrome was referred to the authors’ institute for surgical assessment. Physical examination showed a severe symmetric pectus excavatum, with a Haller Index of 7.8. Preoperative workup included a transesophageal echocardiography that revealed severe mitral valve regurgitation due to bileaflet mitral valve prolapse and a 5 cm aortic root dilatation involving the sinuses of Valsalva. The aortic valve was tricuspid and no alterations in flow were observed. A single-stage surgical repair of pectus excavatum and congenital heart lesions was recommended.<div>Learn more: https://www.ctsnet.org/article/marfan-syndrome-single-stage-surgical-repair-pectus-excavatum-combined-mitral-valve-repair</div>